Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.
Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance / Di Dato, Fabiola; Spadarella, Simona; Puoti, Maria Giovanna; Caprio, Maria Grazia; Pagliardini, Severo; Zuppaldi, Claudia; Vallone, Gianfranco; Fecarotta, Simona; Esposito, Gabriella; Iorio, Raffaele; Parenti, Giancarlo; Spagnuolo, Maria Immacolata. - In: NUTRIENTS. - ISSN 2072-6643. - 11:10(2019). [10.3390/nu11102397]
Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance
Di Dato, Fabiola;Spadarella, Simona;Puoti, Maria Giovanna;Caprio, Maria Grazia;Vallone, Gianfranco;Fecarotta, Simona;Esposito, Gabriella;Iorio, Raffaele;Parenti, Giancarlo
;Spagnuolo, Maria Immacolata
2019
Abstract
Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.