Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.

Daily Fructose Traces Intake and Liver Injury in Children with Hereditary Fructose Intolerance

Di Dato, Fabiola;Spadarella, Simona;Puoti, Maria Giovanna;Caprio, Maria Grazia;Vallone, Gianfranco;Fecarotta, Simona;Esposito, Gabriella;Iorio, Raffaele;Parenti, Giancarlo
;
Spagnuolo, Maria Immacolata
2019

Abstract

Hereditary fructose intolerance (HFI) is a rare genetic disorder of fructose metabolism due to aldolase B enzyme deficiency. Treatment consists of fructose, sorbitol, and sucrose (FSS)-free diet. We explore possible correlations between daily fructose traces intake and liver injury biomarkers on a long-term period, in a cohort of young patients affected by HFI.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11588/770896
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