SURACE, Enrico Maria
 Distribuzione geografica
Continente #
EU - Europa 1.349
NA - Nord America 1.303
AS - Asia 893
SA - Sud America 185
AF - Africa 22
OC - Oceania 3
Continente sconosciuto - Info sul continente non disponibili 2
Totale 3.757
Nazione #
US - Stati Uniti d'America 1.276
RU - Federazione Russa 606
SG - Singapore 510
IT - Italia 308
BR - Brasile 169
HK - Hong Kong 162
CN - Cina 150
NL - Olanda 85
FI - Finlandia 81
UA - Ucraina 79
DE - Germania 66
IE - Irlanda 36
SE - Svezia 32
CA - Canada 20
VN - Vietnam 18
GB - Regno Unito 17
IN - India 15
FR - Francia 13
BD - Bangladesh 8
ZA - Sudafrica 8
AT - Austria 7
ES - Italia 7
TW - Taiwan 7
MX - Messico 6
KE - Kenya 4
KR - Corea 4
UY - Uruguay 4
AR - Argentina 3
AU - Australia 3
BG - Bulgaria 3
CI - Costa d'Avorio 3
EC - Ecuador 3
PK - Pakistan 3
PL - Polonia 3
TN - Tunisia 3
TR - Turchia 3
UZ - Uzbekistan 3
EU - Europa 2
IQ - Iraq 2
PE - Perù 2
PY - Paraguay 2
SA - Arabia Saudita 2
BH - Bahrain 1
BY - Bielorussia 1
CH - Svizzera 1
CO - Colombia 1
CY - Cipro 1
CZ - Repubblica Ceca 1
DO - Repubblica Dominicana 1
EG - Egitto 1
GA - Gabon 1
JO - Giordania 1
JP - Giappone 1
LT - Lituania 1
LU - Lussemburgo 1
MA - Marocco 1
NP - Nepal 1
PS - Palestinian Territory 1
PT - Portogallo 1
SN - Senegal 1
VE - Venezuela 1
Totale 3.757
Città #
Singapore 315
Chandler 277
Hong Kong 160
Moscow 146
Naples 105
Santa Clara 83
Amsterdam 79
Millbury 70
Princeton 56
Nanjing 54
Jacksonville 48
Ashburn 40
Des Moines 38
Boston 30
Napoli 26
Munich 24
Wilmington 22
Nanchang 18
São Paulo 17
Ann Arbor 16
Helsinki 16
Ottawa 15
Siena 15
Lawrence 13
Shenyang 13
Beijing 12
Dong Ket 12
Jiaxing 12
Nuremberg 10
Hebei 9
Los Angeles 9
Rio de Janeiro 8
Seattle 8
Caserta 7
New York 7
Tianjin 7
Boardman 6
Taichung 6
Dublin 5
New Delhi 5
Turku 5
Benevento 4
Brooklyn 4
Campinas 4
Enna 4
Falkenstein 4
Falls Church 4
Frankfurt am Main 4
Johannesburg 4
Lappeenranta 4
Madrid 4
Marigliano 4
Milan 4
Montevideo 4
Nairobi 4
Redwood City 4
Rome 4
Zhengzhou 4
Curitiba 3
Fairfield 3
Fortaleza 3
Hefei 3
Portsmouth 3
Praia Grande 3
Shanghai 3
Sofia 3
The Dalles 3
Trento 3
Afragola 2
Assis 2
Asunción 2
Betim 2
Chicago 2
Denver 2
Diadema 2
Dourados 2
Guangzhou 2
Hangzhou 2
Hanoi 2
Ho Chi Minh City 2
Indaiatuba 2
Jundiaí 2
Lauterbourg 2
Livorno 2
Matinhos 2
Mexico City 2
Monteviale 2
Norwalk 2
Pindamonhangaba 2
Qualiano 2
Salvador 2
San Diego 2
San Francisco 2
San Jose 2
Springfield 2
São José do Rio Preto 2
Tashkent 2
Toronto 2
Uberlândia 2
Ustaritz 2
Totale 1.986
Nome #
Light-responsive microRNA miR-211 targets Ezrin to modulate lysosomal biogenesis and retinal cell clearance 135
The Ocular Albinism type 1 (OA!) gene controls melanosome maturation and size. 112
The centrosomal OFD1 protein interacts with the translation machinery and regulates the synthesis of specific targets. 90
Sulfatase modifying factor 1 trafficking through the cells: from endoplasmic reticulum to the endoplasmic reticulum. 87
Intein-mediated protein trans-splicing expands adeno-associated virus transfer capacity in the retina 78
AAV-miR-204 Protects from Retinal Degeneration by Attenuation of Microglia Activation and Photoreceptor Cell Death 77
GENE THERAPY FOR LEBER'S CONGENITAL AMAUROSIS IS SAFE AND EFFECTIVE 1.5 YEARS AFTER VECTOR ADMINISTRATION 75
Adeno-associated viral vectors for retinal gene transfer. 74
Access to cerebrospinal fluid in piglets via the cisterna magna: Optimization and description of the technique 71
A comprehensive map of CNS transduction by eight recombinant adeno-associated virus serotypes upon cerebrospinal fluid administration in pigs 69
Systemic but not intraocular Epo gene transfer protects the retina from light- and genetic-induced degeneration. 65
Delivery of adeno-associated virus vectors to the fetal retina: impact of viral capsid proteins on retinal neuronal progenitor transduction. 65
Activation of Melanocortin Receptors MC1 and MC5 Attenuates Retinal Damage in Experimental Diabetic Retinopathy 65
Gene therapy of inherited retinal degenerations: prospects and challenges. 64
SLC7A8, a gene mapping within the lysinuric protein intolerance critical region, encodes a new member of the glycoprotein associated amino acid transporter family. 63
Age-dependent effects of RPE65 gene therapy for Leber's congenital amaurosis: a phase 1 dose-escalation trial. 63
AAV vectors efficiently and stably transduce fetal retina. 62
miR-181a/b downregulation exerts a protective action on mitochondrial disease models 61
Efficacy of a combined intracerebral and systemic gene delivery approach for the treatment of a severe lysosomal storage disorder. 61
Transdermal spinal catheter placement in piglets: Description and validation of the technique. 61
Oa1 knock-out: new insights on the pathogenesis of ocular albinism type 1 60
Pigment epithelium-derived factor expression in the developing mouse eye. 59
Allele-specific editing ameliorates dominant retinitis pigmentosa in a transgenic mouse model 59
TOWARDS CLINICAL TRIALS FOR AAV-MEDIATED EYE- AND LIVER - DIRECT GENE THERAPY TRANSLATION AAV 58
Inclusion of a degron reduces levelsof undesired inteins after AAV-mediated proteintrans-splicing in the retina 58
MiR-211 is essential for adult cone photoreceptor maintenance and visual function 56
Expression pattern of the ocular albinism type 1 (Oa1) gene in the murine retinal pigment epithelium. 54
AP20817-inducible activation of chimeric insulin receptor mimics insulin action in hepatocytes transduced with AAV 54
Gene therapy for Leber's congenital amaurosis is safe and effective through 1.5 years after vector administration. 54
Molecular and clinical characterization of albinism in a large cohort of Italian patients. 54
Therapeutic homology-independent targeted integration in retina and liver 54
AAV-mediated Tyrosinase Gene Transfer Restores Melanogenesis and Retinal Function in a Model of Oculo-cutaneous Albinism Type I (OCA1). 53
Amelioration of both functional and morphological abnormalities in the retina of a mouse model of ocular albinism following AAV-mediated gene transfer. 53
Localization of pigment epithelium derived factor (PEDF) in developing and adult human ocular tissues. 53
Challenging safety and efficacy of retinal gene therapies by retinogenesis 53
Correlation betwen photoreceptor layer integrity and visual function in patients with Stargardt Disease:implication for gene therapy 52
The long noncoding RNA Vax2os1 controls the cell cycle progression of photoreceptor progenitors in the mouse retina. 50
Aberrant splicing in the ocular albinism type 1 gene (OA1/GPR143) is corrected in vitro by morpholino antisense oligonucleotides. 50
The ocular albinism type 1 (OA1) gene controls melanosome maturation and size. 49
The distribution, concentration, and toxicity of enhanced green fluorescent protein in retinal cells after genomic or somatic (virus-mediated) gene transfer. 49
Safety and efficacy of gene transfer for Leber's congenital amaurosis. 49
Mouse embryonic retina delivers information controlling cortical neurogenesis. 49
AAV-mediated photoreceptor transduction of the pig cone-enriched retina 47
Müller cell transduction by AAV2 in normal and degenerative retinas. 47
Recombinant vectors based on porcine adeno-associated viral serotypes transduce the murine and pig retina. 46
Combined rod and cone transduction by AAV2/8. 46
The ocular albinism type 1 protein, an intracellular G protein-coupled receptor, regulates melanosome transport in pigment cells. 46
In utero gene therapy rescues vision in a murine model of congenital blindness. 45
Systemic but not intraocular Epo gene transfer protects the retina from light-and genetic-induced degeneration. 45
Corrigendum to: Sulfatase modifying factor 1 trafficking through the cells: from endoplasmic reticulum to the endoplasmic reticulum (The EMBO Journal, (2007), 26, 10, (2443-2453), 10.1038/sj.emboj.7601695) 45
Inhibition of ocular neovascularization by Hedgehog blockade. 43
The ocular albinism type 1 (OA1) protein, an intracellur G protein-coupled receptor, regulates melanosome transport in pigment cells. 43
Oa1 knock-out: new insights on the pathogenesis of ocular albinism type 1. 43
The ocular albinism type 1 (OA1) G-protein-coupled receptor functions with MART-1 at early stages of melanogenesis to control melanosome identity and composition. 42
Three-year follow-up after unilateral subretinal delivery of adeno-associated virus in patients with Leber congenital Amaurosis type 2. 41
SLC7A8, a gene mapping within the lysinuric protein intolerance critical region, encodes a new member of the glycoprotein-associated amino acid transporter family. 41
Rhodopsin targeted transcriptional silencing by DNA-binding 39
Phenotypic rescue after adeno-associated virus-mediated delivery of 4-sulfatase to the retinal pigment epithelium of feline mucopolysaccharidosis VI. 38
Evaluation of italian patients with Leber Congenital Amaurosis due to AIPL1 mutations highlights the potential applicability of gene therapy 37
Novel adeno-associated virus serotypes efficiently transduce murine photoreceptors. 37
Non-erythropoietic erythropoietin derivatives protect from light-induced and genetic photoreceptor degeneration. 36
Gene therapy for Leber congenital amaurosis. 36
Use of compounds that interfere with the hedghehog signaling pathway for the manufacture of a medicament for preventing, inhibiting 34
Versatility of AAV vectors for retinal gene transfer 33
Zinc-finger-based transcriptional repression of rhodopsin in a model of dominant retinitis pigmentosa 33
Characterization of a WAS splice-site variant in a patient with Wiskott-Aldrich syndrome 30
Targeting and silencing of rhodopsin by ectopic expression of the transcription factor KLF15 30
Artificial DNA-binding proteins and uses thereof 29
Efficacy, pharmacokinetics, and safety in the mouse and primate retina of dual AAV vectors for Usher syndrome type 1B 28
miR-181a/b downregulation: a mutation-independent therapeutic approach for inherited retinal diseases 28
Erratum: The ocular albinism type 1 protein, an intracellular G protein-coupled receptor, regulates melanosome transport in pigment cells (Human molecular genetics (2008) 17 22 (3487-3501)) 27
ECTOPICALLY EXPRESSED TRANSCRIPTION FACTORS AND USES THEREOF 27
Gene replacement therapy provides benefit in an adult mouse model of Leigh syndrome 21
Retinal gene therapy for Stargardt disease with dual AAV intein vectors is both safe and effective in large animal models 11
Totale 3.852
Categoria #
all - tutte 15.583
article - articoli 0
book - libri 0
conference - conferenze 0
curatela - curatele 0
other - altro 0
patent - brevetti 0
selected - selezionate 0
volume - volumi 0
Totale 15.583


Totale Lug Ago Sett Ott Nov Dic Gen Feb Mar Apr Mag Giu
2020/2021173 3 10 21 17 14 20 18 10 21 10 13 16
2021/2022362 8 1 2 8 9 4 23 7 43 40 60 157
2022/2023633 75 50 18 57 85 77 6 54 94 71 38 8
2023/2024373 12 65 102 17 13 22 15 10 3 5 85 24
2024/20251.716 85 112 7 6 36 94 247 110 71 177 625 146
2025/2026176 176 0 0 0 0 0 0 0 0 0 0 0
Totale 3.852