GALIETTA, Luis Juan Vicente
GALIETTA, Luis Juan Vicente
Dipartimento di Scienze mediche traslazionali
Airway surface hyperviscosity and defective mucociliary transport by IL-17/TNF-α are corrected by beta-adrenergic stimulus
2022 Guidone, Daniela; Buccirossi, Martina; Scudieri, Paolo; Genovese, Michele; Sarnataro, Sergio; De Cegli, Rossella; Cresta, Federico; Terlizzi, Vito; Planelles, Gabrielle; Crambert, Gilles; Sermet-Gaudelus, Isabelle; Galietta, Luis Jv
Rescue by elexacaftor-tezacaftor-ivacaftor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell background
2022 Tomati, Valeria; Costa, Stefano; Capurro, Valeria; Pesce, Emanuela; Pastorino, Cristina; Lena, Mariateresa; Sondo, Elvira; Di Duca, Marco; Cresta, Federico; Cristadoro, Simona; Zara, Federico; Galietta, Luis Juan Vicente; Bocciardi, Renata; Castellani, Carlo; Lucanto, Maria Cristina; Pedemonte, Nicoletta
The L467F-F508del Complex Allele Hampers Pharmacological Rescue of Mutant CFTR by Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis Patients: The Value of the Ex Vivo Nasal Epithelial Model to Address Non-Responders to CFTR-Modulating Drugs
2022 Sondo, Elvira; Cresta, Federico; Pastorino, Cristina; Tomati, Valeria; Capurro, Valeria; Pesce, Emanuela; Lena, Mariateresa; Iacomino, Michele; Baffico, Ave Maria; Coviello, Domenico; Bandiera, Tiziano; Zara, Federico; Galietta, L; Bocciardi, Renata; Castellani, Carlo; Pedemonte, Nicoletta
TMEM16A (ANO1) as a therapeutic target in cystic fibrosis
2022 Galietta, L
Isolation, cultivation, and application of primary respiratory epithelial cells obtained by nasal brushing, polyp samples, or lung explants
2022 Golec, Anita; Pranke, Iwona; Scudieri, Paolo; Hayes, Kate; Dreano, Elise; Dunlevy, Fiona; Hatton, Aurelie; Downey, Damian G; Galietta, Luis; Sermet, Isabelle
KCa3.1 differentially regulates trachea and bronchi epithelial gene expression in a chronic-asthma mouse model
2022 Philp, Amber R; Miranda, Fernando; Gianotti, Ambra; Mansilla, Agustín; Scudieri, Paolo; Musante, Ilaria; Vega, Génesis; Figueroa, Carlos D; Galietta, L; Sarmiento, José M; Flores, Carlos A
Pharmacoproteomics pinpoints HSP70 interaction for correction of the most frequent Wilson disease-causing mutant of ATP7B
2020 Concilli, M.; Petruzzelli, R.; Parisi, S.; Catalano, F.; Sirci, F.; Napolitano, F.; Renda, M.; Galietta, L. J. V.; Bernardo, D. D.; Polishchuk, R. S.
Esc peptides as novel potentiators of defective cystic fibrosis transmembrane conductance regulator: an unprecedented property of antimicrobial peptides
2022 Ferrera, L.; Cappiello, F.; Loffredo, M. R.; Puglisi, E.; Casciaro, B.; Botta, B.; Galietta, L. J. V.; Mori, M.; Mangoni, M. L.
Chloride transport modulators as drug candidates
2021 Verkman, Alan S; Galietta, L
Comprehensive analysis of combinatorial pharmacological treatments to correct nonsense mutations in the cftr gene
2021 Venturini, A.; Borrelli, A.; Musante, I.; Scudieri, P.; Capurro, V.; Renda, M.; Pedemonte, N.; Galietta, L. J. V.
Ex vivo model predicted in vivo efficacy of CFTR modulator therapy in a child with rare genotype
2021 Terlizzi, V.; Amato, F.; Castellani, C.; Ferrari, B.; Galietta, L. J. V.; Castaldo, G.; Taccetti, G.
Partial rescue of f508del-cftr stability and trafficking defects by double corrector treatment
2021 Capurro, V.; Tomati, V.; Sondo, E.; Renda, M.; Borrelli, A.; Pastorino, C.; Guidone, D.; Venturini, A.; Giraudo, A.; Bertozzi, S. M.; Musante, I.; Bertozzi, F.; Bandiera, T.; Zara, F.; Galietta, L. J. V.; Pedemonte, N.
Evaluation of Fused Pyrrolothiazole Systems as Correctors of Mutant CFTR Protein
2021 Spano, V.; Barreca, M.; Cilibrasi, V.; Genovese, M.; Renda, M.; Montalbano, A.; Galietta, L. J. V.; Barraja, P.
Pharmacological approaches to cystic fibrosis
2021 Bandiera, T.; Galietta, L. J. V.
Intrinsic Abnormalities of Cystic Fibrosis Airway Connective Tissue Revealed by an In Vitro 3D Stromal Model
2020 Mazio, C.; Scognamiglio, L. S.; Cegli, R.; Galietta, L. J. V.; Bernardo, D. D.; Casale, C.; Urciuolo, F.; Imparato, G.; Netti, P. A.
Identification, Structure-Activity Relationship, and Biological Characterization of 2,3,4,5-Tetrahydro-1H-pyrido[4,3-b]indoles as a Novel Class of CFTR Potentiators
2020 Brindani, Nicoletta; Gianotti, Ambra; Giovani, Simone; Giacomina, Francesca; Di Fruscia, Paolo; Sorana, Federico; Bertozzi, Sine Mandrup; Ottonello, Giuliana; Goldoni, Luca; Penna, Ilaria; Russo, Debora; Summa, Maria; Bertorelli, Rosalia; Ferrera, Loretta; Pesce, Emanuela; Sondo, Elvira; Galietta, Luis Juan Vicente; Bandiera, Tiziano; Pedemonte, Nicoletta; Bertozzi, Fabio
Ionocytes and CFTR Chloride Channel Expression in Normal and Cystic Fibrosis Nasal and Bronchial Epithelial Cells
2020 Scudieri, P.; Musante, I.; Venturini, A.; Guidone, D.; Genovese, M.; Cresta, F.; Caci, E.; Palleschi, A.; Poeta, M.; Santamaria, F.; Ciciriello, F.; Lucidi, V.; Galietta, L. J. V.
Current development of CFTR potentiators in the last decade
2020 Spano, V.; Venturini, A.; Genovese, M.; Barreca, M.; Raimondi, M. V.; Montalbano, A.; Galietta, L. J. V.; Barraja, P.
Lack of Kcnn4 improves mucociliary clearance in muco-obstructive lung disease
2020 Vega, G.; Guequen, A.; Philp, A. R.; Gianotti, A.; Arzola, L.; Villalon, M.; Zegarra-Moran, O.; Galietta, L. J. V.; Mall, M. A.; Flores, C. A.
The role of functional studies in the diagnosis and treatment of Cystic Fibrosis: comparing the case of the G970D and G970R mutation.
2018 Amato, F; Scudieri, P; Musante, I; Tomati, V; Caci, E; Comegna, M; Maietta, S; Manzoni, F; DI LULLO, ANTONELLA MIRIAM; De Wachter, E; Vanderhelst, Eef; Terlizzi, V; Braggion, C; Castaldo, G; Galietta, Ljv.
| Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|---|
| Airway surface hyperviscosity and defective mucociliary transport by IL-17/TNF-α are corrected by beta-adrenergic stimulus | 1.1 Articolo in rivista | 2022 | Guidone, Daniela; Buccirossi, Martina; Scudieri, Paolo; Genovese, Michele; Sarnataro, Sergio; De Cegli, Rossella; Cresta, Federico; Terlizzi, Vito; Planelles, Gabrielle; Crambert, Gilles; Sermet-Gaudelus, Isabelle; Galietta, Luis Jv | |
| Rescue by elexacaftor-tezacaftor-ivacaftor of the G1244E cystic fibrosis mutation's stability and gating defects are dependent on cell background | 1.1 Articolo in rivista | 2022 | Tomati, Valeria; Costa, Stefano; Capurro, Valeria; Pesce, Emanuela; Pastorino, Cristina; Lena, Mariateresa; Sondo, Elvira; Di Duca, Marco; Cresta, Federico; Cristadoro, Simona; Zara, Federico; Galietta, Luis Juan Vicente; Bocciardi, Renata; Castellani, Carlo; Lucanto, Maria Cristina; Pedemonte, Nicoletta | |
| The L467F-F508del Complex Allele Hampers Pharmacological Rescue of Mutant CFTR by Elexacaftor/Tezacaftor/Ivacaftor in Cystic Fibrosis Patients: The Value of the Ex Vivo Nasal Epithelial Model to Address Non-Responders to CFTR-Modulating Drugs | 1.1 Articolo in rivista | 2022 | Sondo, Elvira; Cresta, Federico; Pastorino, Cristina; Tomati, Valeria; Capurro, Valeria; Pesce, Emanuela; Lena, Mariateresa; Iacomino, Michele; Baffico, Ave Maria; Coviello, Domenico; Bandiera, Tiziano; Zara, Federico; Galietta, L; Bocciardi, Renata; Castellani, Carlo; Pedemonte, Nicoletta | |
| TMEM16A (ANO1) as a therapeutic target in cystic fibrosis | 1.2 Recensione in rivista | 2022 | Galietta, L | |
| Isolation, cultivation, and application of primary respiratory epithelial cells obtained by nasal brushing, polyp samples, or lung explants | 1.1 Articolo in rivista | 2022 | Golec, Anita; Pranke, Iwona; Scudieri, Paolo; Hayes, Kate; Dreano, Elise; Dunlevy, Fiona; Hatton, Aurelie; Downey, Damian G; Galietta, Luis; Sermet, Isabelle | |
| KCa3.1 differentially regulates trachea and bronchi epithelial gene expression in a chronic-asthma mouse model | 1.1 Articolo in rivista | 2022 | Philp, Amber R; Miranda, Fernando; Gianotti, Ambra; Mansilla, Agustín; Scudieri, Paolo; Musante, Ilaria; Vega, Génesis; Figueroa, Carlos D; Galietta, L; Sarmiento, José M; Flores, Carlos A | |
| Pharmacoproteomics pinpoints HSP70 interaction for correction of the most frequent Wilson disease-causing mutant of ATP7B | 1.1 Articolo in rivista | 2020 | Concilli, M.; Petruzzelli, R.; Parisi, S.; Catalano, F.; Sirci, F.; Napolitano, F.; Renda, M.; Galietta, L. J. V.; Bernardo, D. D.; Polishchuk, R. S. | |
| Esc peptides as novel potentiators of defective cystic fibrosis transmembrane conductance regulator: an unprecedented property of antimicrobial peptides | 1.1 Articolo in rivista | 2022 | Ferrera, L.; Cappiello, F.; Loffredo, M. R.; Puglisi, E.; Casciaro, B.; Botta, B.; Galietta, L. J. V.; Mori, M.; Mangoni, M. L. | |
| Chloride transport modulators as drug candidates | 1.1 Articolo in rivista | 2021 | Verkman, Alan S; Galietta, L | |
| Comprehensive analysis of combinatorial pharmacological treatments to correct nonsense mutations in the cftr gene | 1.1 Articolo in rivista | 2021 | Venturini, A.; Borrelli, A.; Musante, I.; Scudieri, P.; Capurro, V.; Renda, M.; Pedemonte, N.; Galietta, L. J. V. | |
| Ex vivo model predicted in vivo efficacy of CFTR modulator therapy in a child with rare genotype | 1.1 Articolo in rivista | 2021 | Terlizzi, V.; Amato, F.; Castellani, C.; Ferrari, B.; Galietta, L. J. V.; Castaldo, G.; Taccetti, G. | |
| Partial rescue of f508del-cftr stability and trafficking defects by double corrector treatment | 1.1 Articolo in rivista | 2021 | Capurro, V.; Tomati, V.; Sondo, E.; Renda, M.; Borrelli, A.; Pastorino, C.; Guidone, D.; Venturini, A.; Giraudo, A.; Bertozzi, S. M.; Musante, I.; Bertozzi, F.; Bandiera, T.; Zara, F.; Galietta, L. J. V.; Pedemonte, N. | |
| Evaluation of Fused Pyrrolothiazole Systems as Correctors of Mutant CFTR Protein | 1.1 Articolo in rivista | 2021 | Spano, V.; Barreca, M.; Cilibrasi, V.; Genovese, M.; Renda, M.; Montalbano, A.; Galietta, L. J. V.; Barraja, P. | |
| Pharmacological approaches to cystic fibrosis | 1.1 Articolo in rivista | 2021 | Bandiera, T.; Galietta, L. J. V. | |
| Intrinsic Abnormalities of Cystic Fibrosis Airway Connective Tissue Revealed by an In Vitro 3D Stromal Model | 1.1 Articolo in rivista | 2020 | Mazio, C.; Scognamiglio, L. S.; Cegli, R.; Galietta, L. J. V.; Bernardo, D. D.; Casale, C.; Urciuolo, F.; Imparato, G.; Netti, P. A. | |
| Identification, Structure-Activity Relationship, and Biological Characterization of 2,3,4,5-Tetrahydro-1H-pyrido[4,3-b]indoles as a Novel Class of CFTR Potentiators | 1.1 Articolo in rivista | 2020 | Brindani, Nicoletta; Gianotti, Ambra; Giovani, Simone; Giacomina, Francesca; Di Fruscia, Paolo; Sorana, Federico; Bertozzi, Sine Mandrup; Ottonello, Giuliana; Goldoni, Luca; Penna, Ilaria; Russo, Debora; Summa, Maria; Bertorelli, Rosalia; Ferrera, Loretta; Pesce, Emanuela; Sondo, Elvira; Galietta, Luis Juan Vicente; Bandiera, Tiziano; Pedemonte, Nicoletta; Bertozzi, Fabio | |
| Ionocytes and CFTR Chloride Channel Expression in Normal and Cystic Fibrosis Nasal and Bronchial Epithelial Cells | 1.1 Articolo in rivista | 2020 | Scudieri, P.; Musante, I.; Venturini, A.; Guidone, D.; Genovese, M.; Cresta, F.; Caci, E.; Palleschi, A.; Poeta, M.; Santamaria, F.; Ciciriello, F.; Lucidi, V.; Galietta, L. J. V. | |
| Current development of CFTR potentiators in the last decade | 1.1 Articolo in rivista | 2020 | Spano, V.; Venturini, A.; Genovese, M.; Barreca, M.; Raimondi, M. V.; Montalbano, A.; Galietta, L. J. V.; Barraja, P. | |
| Lack of Kcnn4 improves mucociliary clearance in muco-obstructive lung disease | 1.1 Articolo in rivista | 2020 | Vega, G.; Guequen, A.; Philp, A. R.; Gianotti, A.; Arzola, L.; Villalon, M.; Zegarra-Moran, O.; Galietta, L. J. V.; Mall, M. A.; Flores, C. A. | |
| The role of functional studies in the diagnosis and treatment of Cystic Fibrosis: comparing the case of the G970D and G970R mutation. | 4.2 Abstract in Atti di convegno | 2018 | Amato, F; Scudieri, P; Musante, I; Tomati, V; Caci, E; Comegna, M; Maietta, S; Manzoni, F; DI LULLO, ANTONELLA MIRIAM; De Wachter, E; Vanderhelst, Eef; Terlizzi, V; Braggion, C; Castaldo, G; Galietta, Ljv. |