GRUMATI, Paolo
GRUMATI, Paolo
Dipartimento di Medicina clinica e Chirurgia
Autophagy is Impaired in the Tibialis Anterior of Dystrophin Null Mice
2013 Spitali, Pietro; Grumati, Paolo; Hiller, Monika; Chrisam, Martina; Aartsma-Rus, Annemieke; Bonaldo, Paolo
Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins
2007 Angelin, Alessia; Tiepolo, Tania; Sabatelli, Patrizia; Grumati, Paolo; Bergamin, Natascha; Golfieri, Cristina; Mattioli, Elisabetta; Gualandi, Francesca; Ferlini, Alessandra; Merlini, Luciano; Maraldi, Nadir M; Bonaldo, Paolo; Bernardi, Paolo
Three novel collagen VI chains with high homology to the alpha3 chain
2008 Gara, Sudheer Kumar; Grumati, Paolo; Urciuolo, Anna; Bonaldo, Paolo; Kobbe, Birgit; Koch, Manuel; Paulsson, Mats; Wagener, Raimund
Autosomal recessive myosclerosis myopathy is a collagen VI disorder
2008 Merlini, L; Martoni, E; Grumati, P; Sabatelli, P; Squarzoni, S; Urciuolo, A; Ferlini, A; Gualandi, F; Bonaldo, P
Identification and characterization of novel collagen VI non-canonical splicing mutations causing Ullrich congenital muscular dystrophy
2009 Martoni, Elena; Urciuolo, Anna; Sabatelli, Patrizia; Fabris, Marina; Bovolenta, Matteo; Neri, Marcella; Grumati, Paolo; D'Amico, Adele; Pane, Marika; Mercuri, Eugenio; Bertini, Enrico; Merlini, Luciano; Bonaldo, Paolo; Ferlini, Alessandra; Gualandi, Francesca
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies
2010 Bovolenta, Matteo; Neri, Marcella; Martoni, Elena; Urciuolo, Anna; Sabatelli, Patrizia; Fabris, Marina; Grumati, Paolo; Mercuri, Eugenio; Bertini, Enrico; Merlini, Luciano; Bonaldo, Paolo; Ferlini, Alessandra; Gualandi, Francesca
Expression of the collagen VI α5 and α6 chains in normal human skin and in skin of patients with collagen VI-related myopathies
2011 Sabatelli, Patrizia; Gara, Sudheer K; Grumati, Paolo; Urciuolo, Anna; Gualandi, Francesca; Curci, Rosa; Squarzoni, Stefano; Zamparelli, Alessandra; Martoni, Elena; Merlini, Luciano; Paulsson, Mats; Bonaldo, Paolo; Wagener, Raimund
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration
2010 Grumati, Paolo; Coletto, Luisa; Sabatelli, Patrizia; Cescon, Matilde; Angelin, Alessia; Bertaggia, Enrico; Blaauw, Bert; Urciuolo, Anna; Tiepolo, Tania; Merlini, Luciano; Maraldi, Nadir M; Bernardi, Paolo; Sandri, Marco; Bonaldo, Paolo
Differential and restricted expression of novel collagen VI chains in mouse
2011 Gara, Sudheer Kumar; Grumati, Paolo; Squarzoni, Stefano; Sabatelli, Patrizia; Urciuolo, Anna; Bonaldo, Paolo; Paulsson, Mats; Wagener, Raimund
Autophagy induction rescues muscular dystrophy
2011 Grumati, Paolo; Coletto, Luisa; Sandri, Marco; Bonaldo, Paolo
Physical exercise stimulates autophagy in normal skeletal muscles but is detrimental for collagen VI-deficient muscles
2011 Grumati, Paolo; Coletto, Luisa; Schiavinato, Alvise; Castagnaro, Silvia; Bertaggia, Enrico; Sandri, Marco; Bonaldo, Paolo
Cyclosporine A in Ullrich congenital muscular dystrophy: long-term results
2011 Merlini, Luciano; Sabatelli, Patrizia; Armaroli, Annarita; Gnudi, Saverio; Angelin, Alessia; Grumati, Paolo; Michelini, Maria Elena; Franchella, Andrea; Gualandi, Francesca; Bertini, Enrico; Maraldi, Nadir Mario; Ferlini, Alessandra; Bonaldo, Paolo; Bernardi, Paolo
Changes in muscle cell metabolism and mechanotransduction are associated with myopathic phenotype in a mouse model of collagen VI deficiency
2013 De Palma, Sara; Leone, Roberta; Grumati, Paolo; Vasso, Michele; Polishchuk, Roman; Capitanio, Daniele; Braghetta, Paola; Bernardi, Paolo; Bonaldo, Paolo; Gelfi, Cecilia
Autophagy in skeletal muscle homeostasis and in muscular dystrophies
2012 Grumati, Paolo; Bonaldo, Paolo
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis
2012 Sabatelli, Patrizia; Gualandi, Francesca; Gara, Sudheer Kumar; Grumati, Paolo; Zamparelli, Alessandra; Martoni, Elena; Pellegrini, Camilla; Merlini, Luciano; Ferlini, Alessandra; Bonaldo, Paolo; Maraldi, Nadir Mario; Paulsson, Mats; Squarzoni, Stefano; Wagener, Raimund
Collagen VI regulates satellite cell self-renewal and muscle regeneration
2013 Urciuolo, Anna; Quarta, Marco; Morbidoni, Valeria; Gattazzo, Francesca; Molon, Sibilla; Grumati, Paolo; Montemurro, Francesca; Tedesco, Francesco Saverio; Blaauw, Bert; Cossu, Giulio; Vozzi, Giovanni; Rando, Thomas A; Bonaldo, Paolo
Skeletal muscle, autophagy, and physical activity: the ménage à trois of metabolic regulation in health and disease
2014 Vainshtein, Anna; Grumati, Paolo; Sandri, Marco; Bonaldo, Paolo
Misregulation of autophagy and protein degradation systems in myopathies and muscular dystrophies
2013 Sandri, Marco; Coletto, Luisa; Grumati, Paolo; Bonaldo, Paolo
Cardiac glycoside ouabain induces autophagic cell death in non-small cell lung cancer cells via a JNK-dependent decrease of Bcl-2
2014 Trenti, Annalisa; Grumati, Paolo; Cusinato, Federico; Orso, Genny; Bonaldo, Paolo; Trevisi, Lucia
S-nitrosoglutathione reductase deficiency-induced S-nitrosylation results in neuromuscular dysfunction
2014 Montagna, Costanza; Di Giacomo, Giuseppina; Rizza, Salvatore; Cardaci, Simone; Ferraro, Elisabetta; Grumati, Paolo; De Zio, Daniela; Maiani, Emiliano; Muscoli, Carolina; Lauro, Filomena; Ilari, Sara; Bernardini, Sergio; Cannata, Stefano; Gargioli, Cesare; Ciriolo, Maria R; Cecconi, Francesco; Bonaldo, Paolo; Filomeni, Giuseppe
Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
---|---|---|---|---|
Autophagy is Impaired in the Tibialis Anterior of Dystrophin Null Mice | 1.1 Articolo in rivista | 2013 | Spitali, Pietro; Grumati, Paolo; Hiller, Monika; Chrisam, Martina; Aartsma-Rus, Annemieke; Bonaldo, Paolo | |
Mitochondrial dysfunction in the pathogenesis of Ullrich congenital muscular dystrophy and prospective therapy with cyclosporins | 1.1 Articolo in rivista | 2007 | Angelin, Alessia; Tiepolo, Tania; Sabatelli, Patrizia; Grumati, Paolo; Bergamin, Natascha; Golfieri, Cristina; Mattioli, Elisabetta; Gualandi, Francesca; Ferlini, Alessandra; Merlini, Luciano; Maraldi, Nadir M; Bonaldo, Paolo; Bernardi, Paolo | |
Three novel collagen VI chains with high homology to the alpha3 chain | 1.1 Articolo in rivista | 2008 | Gara, Sudheer Kumar; Grumati, Paolo; Urciuolo, Anna; Bonaldo, Paolo; Kobbe, Birgit; Koch, Manuel; Paulsson, Mats; Wagener, Raimund | |
Autosomal recessive myosclerosis myopathy is a collagen VI disorder | 1.1 Articolo in rivista | 2008 | Merlini, L; Martoni, E; Grumati, P; Sabatelli, P; Squarzoni, S; Urciuolo, A; Ferlini, A; Gualandi, F; Bonaldo, P | |
Identification and characterization of novel collagen VI non-canonical splicing mutations causing Ullrich congenital muscular dystrophy | 1.1 Articolo in rivista | 2009 | Martoni, Elena; Urciuolo, Anna; Sabatelli, Patrizia; Fabris, Marina; Bovolenta, Matteo; Neri, Marcella; Grumati, Paolo; D'Amico, Adele; Pane, Marika; Mercuri, Eugenio; Bertini, Enrico; Merlini, Luciano; Bonaldo, Paolo; Ferlini, Alessandra; Gualandi, Francesca | |
Identification of a deep intronic mutation in the COL6A2 gene by a novel custom oligonucleotide CGH array designed to explore allelic and genetic heterogeneity in collagen VI-related myopathies | 1.1 Articolo in rivista | 2010 | Bovolenta, Matteo; Neri, Marcella; Martoni, Elena; Urciuolo, Anna; Sabatelli, Patrizia; Fabris, Marina; Grumati, Paolo; Mercuri, Eugenio; Bertini, Enrico; Merlini, Luciano; Bonaldo, Paolo; Ferlini, Alessandra; Gualandi, Francesca | |
Expression of the collagen VI α5 and α6 chains in normal human skin and in skin of patients with collagen VI-related myopathies | 1.1 Articolo in rivista | 2011 | Sabatelli, Patrizia; Gara, Sudheer K; Grumati, Paolo; Urciuolo, Anna; Gualandi, Francesca; Curci, Rosa; Squarzoni, Stefano; Zamparelli, Alessandra; Martoni, Elena; Merlini, Luciano; Paulsson, Mats; Bonaldo, Paolo; Wagener, Raimund | |
Autophagy is defective in collagen VI muscular dystrophies, and its reactivation rescues myofiber degeneration | 1.1 Articolo in rivista | 2010 | Grumati, Paolo; Coletto, Luisa; Sabatelli, Patrizia; Cescon, Matilde; Angelin, Alessia; Bertaggia, Enrico; Blaauw, Bert; Urciuolo, Anna; Tiepolo, Tania; Merlini, Luciano; Maraldi, Nadir M; Bernardi, Paolo; Sandri, Marco; Bonaldo, Paolo | |
Differential and restricted expression of novel collagen VI chains in mouse | 1.1 Articolo in rivista | 2011 | Gara, Sudheer Kumar; Grumati, Paolo; Squarzoni, Stefano; Sabatelli, Patrizia; Urciuolo, Anna; Bonaldo, Paolo; Paulsson, Mats; Wagener, Raimund | |
Autophagy induction rescues muscular dystrophy | 1.1 Articolo in rivista | 2011 | Grumati, Paolo; Coletto, Luisa; Sandri, Marco; Bonaldo, Paolo | |
Physical exercise stimulates autophagy in normal skeletal muscles but is detrimental for collagen VI-deficient muscles | 1.1 Articolo in rivista | 2011 | Grumati, Paolo; Coletto, Luisa; Schiavinato, Alvise; Castagnaro, Silvia; Bertaggia, Enrico; Sandri, Marco; Bonaldo, Paolo | |
Cyclosporine A in Ullrich congenital muscular dystrophy: long-term results | 1.1 Articolo in rivista | 2011 | Merlini, Luciano; Sabatelli, Patrizia; Armaroli, Annarita; Gnudi, Saverio; Angelin, Alessia; Grumati, Paolo; Michelini, Maria Elena; Franchella, Andrea; Gualandi, Francesca; Bertini, Enrico; Maraldi, Nadir Mario; Ferlini, Alessandra; Bonaldo, Paolo; Bernardi, Paolo | |
Changes in muscle cell metabolism and mechanotransduction are associated with myopathic phenotype in a mouse model of collagen VI deficiency | 1.1 Articolo in rivista | 2013 | De Palma, Sara; Leone, Roberta; Grumati, Paolo; Vasso, Michele; Polishchuk, Roman; Capitanio, Daniele; Braghetta, Paola; Bernardi, Paolo; Bonaldo, Paolo; Gelfi, Cecilia | |
Autophagy in skeletal muscle homeostasis and in muscular dystrophies | 1.1 Articolo in rivista | 2012 | Grumati, Paolo; Bonaldo, Paolo | |
Expression of collagen VI α5 and α6 chains in human muscle and in Duchenne muscular dystrophy-related muscle fibrosis | 1.1 Articolo in rivista | 2012 | Sabatelli, Patrizia; Gualandi, Francesca; Gara, Sudheer Kumar; Grumati, Paolo; Zamparelli, Alessandra; Martoni, Elena; Pellegrini, Camilla; Merlini, Luciano; Ferlini, Alessandra; Bonaldo, Paolo; Maraldi, Nadir Mario; Paulsson, Mats; Squarzoni, Stefano; Wagener, Raimund | |
Collagen VI regulates satellite cell self-renewal and muscle regeneration | 1.1 Articolo in rivista | 2013 | Urciuolo, Anna; Quarta, Marco; Morbidoni, Valeria; Gattazzo, Francesca; Molon, Sibilla; Grumati, Paolo; Montemurro, Francesca; Tedesco, Francesco Saverio; Blaauw, Bert; Cossu, Giulio; Vozzi, Giovanni; Rando, Thomas A; Bonaldo, Paolo | |
Skeletal muscle, autophagy, and physical activity: the ménage à trois of metabolic regulation in health and disease | 1.1 Articolo in rivista | 2014 | Vainshtein, Anna; Grumati, Paolo; Sandri, Marco; Bonaldo, Paolo | |
Misregulation of autophagy and protein degradation systems in myopathies and muscular dystrophies | 1.1 Articolo in rivista | 2013 | Sandri, Marco; Coletto, Luisa; Grumati, Paolo; Bonaldo, Paolo | |
Cardiac glycoside ouabain induces autophagic cell death in non-small cell lung cancer cells via a JNK-dependent decrease of Bcl-2 | 1.1 Articolo in rivista | 2014 | Trenti, Annalisa; Grumati, Paolo; Cusinato, Federico; Orso, Genny; Bonaldo, Paolo; Trevisi, Lucia | |
S-nitrosoglutathione reductase deficiency-induced S-nitrosylation results in neuromuscular dysfunction | 1.1 Articolo in rivista | 2014 | Montagna, Costanza; Di Giacomo, Giuseppina; Rizza, Salvatore; Cardaci, Simone; Ferraro, Elisabetta; Grumati, Paolo; De Zio, Daniela; Maiani, Emiliano; Muscoli, Carolina; Lauro, Filomena; Ilari, Sara; Bernardini, Sergio; Cannata, Stefano; Gargioli, Cesare; Ciriolo, Maria R; Cecconi, Francesco; Bonaldo, Paolo; Filomeni, Giuseppe |