Hailey-Hailey disease (HHD) also known as familial benign chronic pemphigus is a rare autoso-mal dominant genodermatosis. HHD treatment is often not satisfactory and hence, variousmodalities of treatment have been tried. We describe the case of a 37-year-old woman with a2 years history of macerated erythematous plaques along with erosions, fissures, and crustslocated on axillae and submammary areas, successfully treated with only oral supplementationof vitamin D (800 I.U./die) for 3 months. We reported this case to suggest that oral vitamin Dmay be enumerated in the various treatments proposed for HHD so far due to its rapid efficacyon skin lesions and symptoms.

Hailey-Hailey disease successfully treated with vitamin D oral supplementation / Megna, Matteo; Scalvenzi, Massimiliano; Russo, Daniela; Timoshchuk, Elena A.; Costa, Claudia; Santoianni, Pietro. - In: DERMATOLOGIC THERAPY. - ISSN 1396-0296. - 32:1(2019), p. e12767. [10.1111/dth.12767]

Hailey-Hailey disease successfully treated with vitamin D oral supplementation

Megna, Matteo
;
Scalvenzi, Massimiliano;Russo, Daniela;Costa, Claudia;Santoianni, Pietro
2019

Abstract

Hailey-Hailey disease (HHD) also known as familial benign chronic pemphigus is a rare autoso-mal dominant genodermatosis. HHD treatment is often not satisfactory and hence, variousmodalities of treatment have been tried. We describe the case of a 37-year-old woman with a2 years history of macerated erythematous plaques along with erosions, fissures, and crustslocated on axillae and submammary areas, successfully treated with only oral supplementationof vitamin D (800 I.U./die) for 3 months. We reported this case to suggest that oral vitamin Dmay be enumerated in the various treatments proposed for HHD so far due to its rapid efficacyon skin lesions and symptoms.
2019
Hailey-Hailey disease successfully treated with vitamin D oral supplementation / Megna, Matteo; Scalvenzi, Massimiliano; Russo, Daniela; Timoshchuk, Elena A.; Costa, Claudia; Santoianni, Pietro. - In: DERMATOLOGIC THERAPY. - ISSN 1396-0296. - 32:1(2019), p. e12767. [10.1111/dth.12767]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11588/740266
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