Chordoma of thoracic vertebras is a very rare locally invasive neoplasm with low grade malignancy arising from embryonic notochordal remnants. Radical surgery remains the cornerstone of the treatment. We describe a case of multifocal T1-T2 chordoma, without bone and disc involvement, incidentally misdiagnosed as a paraganglioma, occurring in a 47-year-old male asymptomatic patient. Neoplasm was radically removed by an endocrine surgeon through a right extended cervicotomy. A preoperative reliable diagnosis of chordoma, as in the reported case, is often difficult. Radical surgery can provide a favorable outcome but, given the high rates of local recurrence of this neoplasm, a strict and careful follow-up is recommended. Although very rare, chordoma should be suggested in the differential diagnosis of the paravertebral cervical masses of unknown origin. Spine surgeon consultation and a FNB should be routinely included in the multidisciplinary preoperative work-up of these neoplasms.

Multifocal thoracic chordoma mimicking a paraganglioma / Conzo, Giovanni; Gambardella, C; Pasquali, D; Ciancia, G; Avenia, N; Pietra, Cd; Napolitano, S; Palazzo, A; Mauriello, C; Parmeggiani, D; Pettinato, Guido; Napolitano, V; Santini, Luigi. - In: JOURNAL OF CANCER RESEARCH AND THERAPEUTICS. - ISSN 0973-1482. - 9:3(2013), pp. 497-499. [10.4103/0973-1482.119312]

Multifocal thoracic chordoma mimicking a paraganglioma.

CONZO, GIOVANNI;PETTINATO, GUIDO;SANTINI, LUIGI
2013

Abstract

Chordoma of thoracic vertebras is a very rare locally invasive neoplasm with low grade malignancy arising from embryonic notochordal remnants. Radical surgery remains the cornerstone of the treatment. We describe a case of multifocal T1-T2 chordoma, without bone and disc involvement, incidentally misdiagnosed as a paraganglioma, occurring in a 47-year-old male asymptomatic patient. Neoplasm was radically removed by an endocrine surgeon through a right extended cervicotomy. A preoperative reliable diagnosis of chordoma, as in the reported case, is often difficult. Radical surgery can provide a favorable outcome but, given the high rates of local recurrence of this neoplasm, a strict and careful follow-up is recommended. Although very rare, chordoma should be suggested in the differential diagnosis of the paravertebral cervical masses of unknown origin. Spine surgeon consultation and a FNB should be routinely included in the multidisciplinary preoperative work-up of these neoplasms.
2013
Multifocal thoracic chordoma mimicking a paraganglioma / Conzo, Giovanni; Gambardella, C; Pasquali, D; Ciancia, G; Avenia, N; Pietra, Cd; Napolitano, S; Palazzo, A; Mauriello, C; Parmeggiani, D; Pettinato, Guido; Napolitano, V; Santini, Luigi. - In: JOURNAL OF CANCER RESEARCH AND THERAPEUTICS. - ISSN 0973-1482. - 9:3(2013), pp. 497-499. [10.4103/0973-1482.119312]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11588/573046
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