Sfoglia per Autore
Lack of Kcnn4 improves mucociliary clearance in muco-obstructive lung disease
2020 Vega, G.; Guequen, A.; Philp, A. R.; Gianotti, A.; Arzola, L.; Villalon, M.; Zegarra-Moran, O.; Galietta, L. J. V.; Mall, M. A.; Flores, C. A.
Ionocytes and CFTR Chloride Channel Expression in Normal and Cystic Fibrosis Nasal and Bronchial Epithelial Cells
2020 Scudieri, P.; Musante, I.; Venturini, A.; Guidone, D.; Genovese, M.; Cresta, F.; Caci, E.; Palleschi, A.; Poeta, M.; Santamaria, F.; Ciciriello, F.; Lucidi, V.; Galietta, L. J. V.
Current development of CFTR potentiators in the last decade
2020 Spano, V.; Venturini, A.; Genovese, M.; Barreca, M.; Raimondi, M. V.; Montalbano, A.; Galietta, L. J. V.; Barraja, P.
Pharmacoproteomics pinpoints HSP70 interaction for correction of the most frequent Wilson disease-causing mutant of ATP7B
2020 Concilli, M.; Petruzzelli, R.; Parisi, S.; Catalano, F.; Sirci, F.; Napolitano, F.; Renda, M.; Galietta, L. J. V.; Bernardo, D. D.; Polishchuk, R. S.
Light-responsive microRNA miR-211 targets Ezrin to modulate lysosomal biogenesis and retinal cell clearance
2020 Naso, Federica; Intartaglia, Daniela; Falanga, Danila; Soldati, Chiara; Polishchuk, Elena; Giamundo, Giuliana; Tiberi, Paola; Marrocco, Elena; Scudieri, Paolo; Di Malta, Chiara; Trapani, Ivana; Nusco, Edoardo; Salierno, Francesco Giuseppe; Surace, Enrico Maria; Galietta, Luis Jv; Banfi, Sandro; Auricchio, Alberto; Ballabio, Andrea; Medina, Diego Luis; Conte, Ivan
Intrinsic Abnormalities of Cystic Fibrosis Airway Connective Tissue Revealed by an In Vitro 3D Stromal Model
2020 Mazio, C.; Scognamiglio, L. S.; Cegli, R.; Galietta, L. J. V.; Bernardo, D. D.; Casale, C.; Urciuolo, F.; Imparato, G.; Netti, P. A.
Identification, Structure-Activity Relationship, and Biological Characterization of 2,3,4,5-Tetrahydro-1H-pyrido[4,3-b]indoles as a Novel Class of CFTR Potentiators
2020 Brindani, Nicoletta; Gianotti, Ambra; Giovani, Simone; Giacomina, Francesca; Di Fruscia, Paolo; Sorana, Federico; Bertozzi, Sine Mandrup; Ottonello, Giuliana; Goldoni, Luca; Penna, Ilaria; Russo, Debora; Summa, Maria; Bertorelli, Rosalia; Ferrera, Loretta; Pesce, Emanuela; Sondo, Elvira; Galietta, Luis Juan Vicente; Bandiera, Tiziano; Pedemonte, Nicoletta; Bertozzi, Fabio
An overview on chemical structures as ΔF508-CFTR correctors
2019 Spano, V.; Montalbano, A.; Carbone, A.; Scudieri, P.; Galietta, L. J. V.; Barraja, P.
Airway microenvironment alterations and pathogen growth in cystic fibrosis
2019 Rossi, Giovanni A.; Morelli, Patrizia; Galietta, Luis J.; Rogers, COLIN ANDREW
TRPV4 and purinergic receptor signalling pathways are separately linked in airway epithelia to CFTR and TMEM16A chloride channels
2019 Genovese, M.; Borrelli, Alessio; Venturini, A.; Guidone, D.; Caci, E.; Viscido, G.; Gambardella, G.; di Bernardo, D.; Scudieri, P.; Galietta, L. J. V.
Furocoumarins as multi-target agents in the treatment of cystic fibrosis
2019 Carbone, A.; Montalbano, A.; Spano, V.; Musante, I.; Galietta, L. J. V.; Barraja, P.
ANO4 (Anoctamin 4) Is a Novel Marker of Zona Glomerulosa That Regulates Stimulated Aldosterone Secretion
2019 Maniero, C.; Scudieri, P.; Haris Shaikh, L.; Zhao, W.; Gurnell, M.; Galietta, L. J. V.; Brown, M. J.
Normal calcium-activated anion secretion in a mouse selectively lacking TMEM16A in intestinal epithelium
2019 Vega, G.; Guequen, A.; Johansson, M. E. V.; Arike, L.; Martinez-Abad, B.; Scudieri, P.; Pedemonte, N.; Millar-Buchner, P.; Philp, A. R.; Galietta, L. J.; Hansson, G. C.; Flores, C. A.
Erratum: Corrigendum Thymosin α-1 does not correct F508del-CFTR in cystic fibrosis airway epithelia (JCI Insight (2018) 3:3 (e98699) DOI: 10.1172/jci.insight.98699)
2019 Tomati, V.; Caci, E.; Ferrera, L.; Pesce, E.; Sondo, E.; Cholon, D. M.; Quinney, N. L.; Boyles, S. E.; Armirotti, A.; Ravazzolo, R.; Galietta, L. J. V.; Gentzsch, M.; Pedemonte, N.
Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis
2019 Simonin, J.; Bille, E.; Crambert, G.; Noel, S.; Dreano, E.; Edwards, A.; Hatton, A.; Pranke, I.; Villeret, B.; Cottart, C. -H.; Vrel, J. -P.; Urbach, V.; Baatallah, N.; Hinzpeter, A.; Golec, A.; Touqui, L.; Nassif, X.; Galietta, L. J. V.; Planelles, G.; Sallenave, J. -M.; Edelman, A.; Sermet-Gaudelus, I.
Corrigendum: Normal calcium-activated anion secretion in a mouse selectively lacking tmem16a in intestinal epithelium (Front. Physiol. 10, 694, 10.3389/fphys.2019.00694)
2019 Vega, G.; Guequen, A.; Johansson, M. E. V.; Arike, L.; Martinez-Abad, B.; Nystrom, E. E. L.; Scudieri, P.; Pedemonte, N.; Millar-Buchner, P.; Philp, A. R.; Galietta, L. J.; Hansson, G. C.; Flores, C. A.
Author Correction: Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis (Scientific Reports, (2019), 9, 1, (6516), 10.1038/s41598-019-42751-4)
2019 Simonin, J.; Bille, E.; Crambert, G.; Noel, S.; Dreano, E.; Edwards, A.; Hatton, A.; Pranke, I.; Villeret, B.; Cottart, C. -H.; Vrel, J. -P.; Urbach, V.; Baatallah, N.; Hinzpeter, A.; Golec, A.; Touqui, L.; Nassif, X.; Galietta, L. J. V.; Planelles, G.; Sallenave, J. -M.; Edelman, A.; Sermet-Gaudelus, I.
Bioactive Thymosin Alpha-1 Does Not Influence F508del-CFTR Maturation and Activity
2019 Armirotti, A.; Tomati, V.; Matthes, E.; Veit, G.; Cholon, D. M.; Phuan, P. -W.; Braccia, Giuseppe; Guidone, D.; Gentzsch, M.; Lukacs, G. L.; Verkman, A. S.; Galietta, L. J. V.; Hanrahan, J. W.; LUZ PEDEMONTE, Benjiamin
High-Throughput Screening for Modulators of CFTR Activity Based on Genetically Engineered Cystic Fibrosis Disease-Specific iPSCs
2019 Merkert, S.; Schubert, M.; Olmer, R.; Engels, L.; Radetzki, S.; Veltman, M.; Scholte, B. J.; Zollner, J.; Pedemonte, N.; Galietta, L. J. V.; von Kries, J. P.; Martin, U.
Peripheral localization of the epithelial sodium channel in the apical membrane of bronchial epithelial cells
2019 Musante, I.; Scudieri, P.; Venturini, A.; Guidone, D.; Caci, E.; Castellani, S.; Conese, M.; Galietta, L. J. V.
Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
---|---|---|---|---|
Lack of Kcnn4 improves mucociliary clearance in muco-obstructive lung disease | 1.1 Articolo in rivista | 2020 | Vega, G.; Guequen, A.; Philp, A. R.; Gianotti, A.; Arzola, L.; Villalon, M.; Zegarra-Moran, O.; Galietta, L. J. V.; Mall, M. A.; Flores, C. A. | |
Ionocytes and CFTR Chloride Channel Expression in Normal and Cystic Fibrosis Nasal and Bronchial Epithelial Cells | 1.1 Articolo in rivista | 2020 | Scudieri, P.; Musante, I.; Venturini, A.; Guidone, D.; Genovese, M.; Cresta, F.; Caci, E.; Palleschi, A.; Poeta, M.; Santamaria, F.; Ciciriello, F.; Lucidi, V.; Galietta, L. J. V. | |
Current development of CFTR potentiators in the last decade | 1.1 Articolo in rivista | 2020 | Spano, V.; Venturini, A.; Genovese, M.; Barreca, M.; Raimondi, M. V.; Montalbano, A.; Galietta, L. J. V.; Barraja, P. | |
Pharmacoproteomics pinpoints HSP70 interaction for correction of the most frequent Wilson disease-causing mutant of ATP7B | 1.1 Articolo in rivista | 2020 | Concilli, M.; Petruzzelli, R.; Parisi, S.; Catalano, F.; Sirci, F.; Napolitano, F.; Renda, M.; Galietta, L. J. V.; Bernardo, D. D.; Polishchuk, R. S. | |
Light-responsive microRNA miR-211 targets Ezrin to modulate lysosomal biogenesis and retinal cell clearance | 1.1 Articolo in rivista | 2020 | Naso, Federica; Intartaglia, Daniela; Falanga, Danila; Soldati, Chiara; Polishchuk, Elena; Giamundo, Giuliana; Tiberi, Paola; Marrocco, Elena; Scudieri, Paolo; Di Malta, Chiara; Trapani, Ivana; Nusco, Edoardo; Salierno, Francesco Giuseppe; Surace, Enrico Maria; Galietta, Luis Jv; Banfi, Sandro; Auricchio, Alberto; Ballabio, Andrea; Medina, Diego Luis; Conte, Ivan | |
Intrinsic Abnormalities of Cystic Fibrosis Airway Connective Tissue Revealed by an In Vitro 3D Stromal Model | 1.1 Articolo in rivista | 2020 | Mazio, C.; Scognamiglio, L. S.; Cegli, R.; Galietta, L. J. V.; Bernardo, D. D.; Casale, C.; Urciuolo, F.; Imparato, G.; Netti, P. A. | |
Identification, Structure-Activity Relationship, and Biological Characterization of 2,3,4,5-Tetrahydro-1H-pyrido[4,3-b]indoles as a Novel Class of CFTR Potentiators | 1.1 Articolo in rivista | 2020 | Brindani, Nicoletta; Gianotti, Ambra; Giovani, Simone; Giacomina, Francesca; Di Fruscia, Paolo; Sorana, Federico; Bertozzi, Sine Mandrup; Ottonello, Giuliana; Goldoni, Luca; Penna, Ilaria; Russo, Debora; Summa, Maria; Bertorelli, Rosalia; Ferrera, Loretta; Pesce, Emanuela; Sondo, Elvira; Galietta, Luis Juan Vicente; Bandiera, Tiziano; Pedemonte, Nicoletta; Bertozzi, Fabio | |
An overview on chemical structures as ΔF508-CFTR correctors | 1.1 Articolo in rivista | 2019 | Spano, V.; Montalbano, A.; Carbone, A.; Scudieri, P.; Galietta, L. J. V.; Barraja, P. | |
Airway microenvironment alterations and pathogen growth in cystic fibrosis | 1.1 Articolo in rivista | 2019 | Rossi, Giovanni A.; Morelli, Patrizia; Galietta, Luis J.; Rogers, COLIN ANDREW | |
TRPV4 and purinergic receptor signalling pathways are separately linked in airway epithelia to CFTR and TMEM16A chloride channels | 1.1 Articolo in rivista | 2019 | Genovese, M.; Borrelli, Alessio; Venturini, A.; Guidone, D.; Caci, E.; Viscido, G.; Gambardella, G.; di Bernardo, D.; Scudieri, P.; Galietta, L. J. V. | |
Furocoumarins as multi-target agents in the treatment of cystic fibrosis | 1.1 Articolo in rivista | 2019 | Carbone, A.; Montalbano, A.; Spano, V.; Musante, I.; Galietta, L. J. V.; Barraja, P. | |
ANO4 (Anoctamin 4) Is a Novel Marker of Zona Glomerulosa That Regulates Stimulated Aldosterone Secretion | 1.1 Articolo in rivista | 2019 | Maniero, C.; Scudieri, P.; Haris Shaikh, L.; Zhao, W.; Gurnell, M.; Galietta, L. J. V.; Brown, M. J. | |
Normal calcium-activated anion secretion in a mouse selectively lacking TMEM16A in intestinal epithelium | 1.1 Articolo in rivista | 2019 | Vega, G.; Guequen, A.; Johansson, M. E. V.; Arike, L.; Martinez-Abad, B.; Scudieri, P.; Pedemonte, N.; Millar-Buchner, P.; Philp, A. R.; Galietta, L. J.; Hansson, G. C.; Flores, C. A. | |
Erratum: Corrigendum Thymosin α-1 does not correct F508del-CFTR in cystic fibrosis airway epithelia (JCI Insight (2018) 3:3 (e98699) DOI: 10.1172/jci.insight.98699) | 1.7 Commento, erratum, replica e simili | 2019 | Tomati, V.; Caci, E.; Ferrera, L.; Pesce, E.; Sondo, E.; Cholon, D. M.; Quinney, N. L.; Boyles, S. E.; Armirotti, A.; Ravazzolo, R.; Galietta, L. J. V.; Gentzsch, M.; Pedemonte, N. | |
Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis | 1.1 Articolo in rivista | 2019 | Simonin, J.; Bille, E.; Crambert, G.; Noel, S.; Dreano, E.; Edwards, A.; Hatton, A.; Pranke, I.; Villeret, B.; Cottart, C. -H.; Vrel, J. -P.; Urbach, V.; Baatallah, N.; Hinzpeter, A.; Golec, A.; Touqui, L.; Nassif, X.; Galietta, L. J. V.; Planelles, G.; Sallenave, J. -M.; Edelman, A.; Sermet-Gaudelus, I. | |
Corrigendum: Normal calcium-activated anion secretion in a mouse selectively lacking tmem16a in intestinal epithelium (Front. Physiol. 10, 694, 10.3389/fphys.2019.00694) | 1.7 Commento, erratum, replica e simili | 2019 | Vega, G.; Guequen, A.; Johansson, M. E. V.; Arike, L.; Martinez-Abad, B.; Nystrom, E. E. L.; Scudieri, P.; Pedemonte, N.; Millar-Buchner, P.; Philp, A. R.; Galietta, L. J.; Hansson, G. C.; Flores, C. A. | |
Author Correction: Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis (Scientific Reports, (2019), 9, 1, (6516), 10.1038/s41598-019-42751-4) | 1.7 Commento, erratum, replica e simili | 2019 | Simonin, J.; Bille, E.; Crambert, G.; Noel, S.; Dreano, E.; Edwards, A.; Hatton, A.; Pranke, I.; Villeret, B.; Cottart, C. -H.; Vrel, J. -P.; Urbach, V.; Baatallah, N.; Hinzpeter, A.; Golec, A.; Touqui, L.; Nassif, X.; Galietta, L. J. V.; Planelles, G.; Sallenave, J. -M.; Edelman, A.; Sermet-Gaudelus, I. | |
Bioactive Thymosin Alpha-1 Does Not Influence F508del-CFTR Maturation and Activity | 1.1 Articolo in rivista | 2019 | Armirotti, A.; Tomati, V.; Matthes, E.; Veit, G.; Cholon, D. M.; Phuan, P. -W.; Braccia, Giuseppe; Guidone, D.; Gentzsch, M.; Lukacs, G. L.; Verkman, A. S.; Galietta, L. J. V.; Hanrahan, J. W.; LUZ PEDEMONTE, Benjiamin | |
High-Throughput Screening for Modulators of CFTR Activity Based on Genetically Engineered Cystic Fibrosis Disease-Specific iPSCs | 1.1 Articolo in rivista | 2019 | Merkert, S.; Schubert, M.; Olmer, R.; Engels, L.; Radetzki, S.; Veltman, M.; Scholte, B. J.; Zollner, J.; Pedemonte, N.; Galietta, L. J. V.; von Kries, J. P.; Martin, U. | |
Peripheral localization of the epithelial sodium channel in the apical membrane of bronchial epithelial cells | 1.1 Articolo in rivista | 2019 | Musante, I.; Scudieri, P.; Venturini, A.; Guidone, D.; Caci, E.; Castellani, S.; Conese, M.; Galietta, L. J. V. |
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