Sfoglia per Autore
Identification of an ultra-rare Alu insertion in the CFTR gene: Pitfalls and challenges in genetic test interpretation
2024 Esposito, Speranza; Zollo, Immacolata; Villella, Valeria Rachela; Scialò, Filippo; Giordano, Sonia; Esposito, Maria Valeria; Salemme, Nunzia; Di Domenico, Carmela; Cernera, Gustavo; Zarrilli, Federica; Castaldo, Giuseppe; Amato, Felice
Collective rotational motion of freely expanding T84 epithelial cell colonies
2023 Ascione, Flora; Caserta, Sergio; Esposito, Speranza; Villella, Valeria Rachela; Maiuri, Luigi; Nejad, Mehrana R; Doostmohammadi, Amin; Yeomans, Julia M; Guido, Stefano
In silico analysis and theratyping of an ultra-rare CFTR genotype (W57G/A234D) in primary human rectal and nasal epithelial cells
2023 Kleinfelder, Karina; Lotti, Virginia; Eramo, Adriana; Amato, Felice; Lo Cicero, Stefania; Castelli, Germana; Spadaro, Francesca; Farinazzo, Alessia; Dell'Orco, Daniele; Preato, Sara; Conti, Jessica; Rodella, Luca; Tomba, Francesco; Cerofolini, Angelo; Baldisseri, Elena; Bertini, Marina; Volpi, Sonia; Villella, Valeria Rachela; Esposito, Speranza; Zollo, Immacolata; Castaldo, Giuseppe; Laudanna, Carlo; Sorsher, Eric J; Hong, Jeong; Joshi, Disha; Cutting, Garry; Lucarelli, Marco; Melotti, Paola; Sorio, Claudio
Immuno-Sensing at Ultra-Low Concentration of TG2 Protein by Organic Electrochemical Transistors
2023 Preziosi, Valentina; Barra, Mario; Villella, VALERIA RACHELA; Esposito, Speranza; D’Angelo, Pasquale; Luigi Marasso, Simone; Cocuzza, Matteo; Cassinese, Antonio; Guido, Stefano
Theratyping of the Rare CFTR Genotype A559T in Rectal Organoids and Nasal Cells Reveals a Relevant Response to Elexacaftor (VX-445) and Tezacaftor (VX-661) Combination
2023 Kleinfelder, K.; Villella, V. R.; Hristodor, A. M.; Laudanna, C.; Castaldo, G.; Amato, F.; Melotti, P.; Sorio, C.
Organic Electrochemical Transistor Immuno-Sensors for Spike Protein Early Detection
2023 Barra, M.; Tomaiuolo, G.; Villella, V. R.; Esposito, S.; Liboa, A.; D'Angelo, P.; Marasso, S. L.; Cocuzza, M.; Bertana, V.; Camilli, E.; Preziosi, V.
Anakinra restores cellular proteostasis by coupling mitochondrial redox balance to autophagy
2022 van de Veerdonk, Frank L; Renga, Giorgia; Pariano, Marilena; Bellet, Marina M; Servillo, Giuseppe; Fallarino, Francesca; De Luca, Antonella; Iannitti, Rossana G; Piobbico, Danilo; Gargaro, Marco; Manni, Giorgia; D'Onofrio, Fiorella; Stincardini, Claudia; Sforna, Luigi; Borghi, Monica; Castelli, Marilena; Pieroni, Stefania; Oikonomou, Vasileios; Villella, Valeria R; Puccetti, Matteo; Giovagnoli, Stefano; Galarini, Roberta; Barola, Carolina; Maiuri, Luigi; Della Fazia, Maria Agnese; Cellini, Barbara; Talesa, Vincenzo Nicola; Dinarello, Charles A; Costantini, Claudio; Romani, Luigina
Probiotics Supplements Reduce ER Stress and Gut Inflammation Associated with Gliadin Intake in a Mouse Model of Gluten Sensitivity.
2021 Ferrari, E; Monzani, R; Saverio, V; Gagliardi, M; Pańczyszyn, E; Raia, V; Villella, Vr; Bona, G; Pane, M; Amoruso, A; Corazzari, M.
Impaired cholesterol metabolism in the mouse model of cystic fibrosis. A preliminary study
2021 Amato, F.; Castaldo, A.; Castaldo, G.; Cernera, G.; Corso, G.; Ferrari, E.; Gelzo, M.; Monzani, R.; Villella, V. R.; Raia, V.
Inhaled medications in cystic fibrosis beyond antibiotics
2019 Sepe, A; Villella, Vr; Cimbalo, C; Castaldo, A; Nunziata, Francesco; Corcione, Adele; Bona, G; Maiuri, L; Raia, V
Defective proteostasis in celiac disease as a new therapeutic target
2019 Maiuri, L; Villella, Vr; Piacentini, Francesco; Raia, V; Kroemer, G; Raia, Valeria
A pathogenic role for cystic fibrosis transmembrane conductance regulator in celiac disease
2019 Villella, Vr; Venerando, A; Cozza, G; Esposito, S; Ferrari, E; Monzani, R; Spinella, Mc; Oikonomou, V; Renga, G; Tosco, A; Rossin, F; Guido, S; Silano, Angelo; Garaci, E; Chao, Yk; Grimm, C; Luciani, A; Romani, L; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L
Cystic fibrosis transmembrane conductance regulator (CFTR) and autophagy: hereditary defects in cystic fibrosis versus gluten-mediated inhibition in celiac disease
2019 Maiuri, L; Raia, V; Piacentini, M; Tosco, A; Villella, Vr; Kroemer, G
Personalization of therapies in rare diseases: a translational approach for the treatment of cystic fibrosis.
2019 Villella, Vr; Tosco, A; Esposito, S; Ferrari, E; Bona, G; Kroemer, G; Raia, V; Maiuri, L
Genistein antagonizes gliadin-induced CFTR malfunction in models of celiac disease.
2019 Esposito, S; Villella, Vr; Ferrari, E; Monzani, R; Tosco, A; Rossin, F; D'Eletto, M; Castaldo, A; Luciani, A; Silano, M; Bona, G; Marseglia, Gl; Romani, L; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L
Autophagy suppresses the pathogenic immune response to dietary antigens in cystic fibrosis.
2019 Villella, Vr; Esposito, S; Ferrari, E; Monzani, R; Tosco, A; Rossin, F; Castaldo, A; Silano, M; Marseglia, Gl; Romani, L; Barlev, Na; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L
Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation
2017 Ferrari, Eleonora; Monzani, Romina; Villella, VALERIA RACHELA; Esposito, Speranza; Saluzzo, Francesca; Rossin, Federica; D'Eletto, Manuela; Tosco, Antonella; DE GREGORIO, Fabiola; Izzo, Valentina; Maiuri, MARIA CHIARA; Kroemer, Guido; Raia, Valeria; Maiuri, Luigi
Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation.
2014 Stefano, Dd; Villella, Vr; Esposito, S; Tosco, A; Sepe, A; De Gregorio, F; Salvadori, L; Grassia, R; Leone, Ca; DE ROSA, Giuseppe; Maiuri, MARIA CHIARA; Pettoello Mantovani, M; Guido, Stefano; Bossi, A; Zolin, A; Venerando, A; Pinna, La; Mehta, A; Bona, G; Kroemer, G; Maiuri, L; Raia, Valeria
Towards a rational combination therapy of cystic fibrosis: How cystamine restores the stability of mutant CFTR
2013 Villella, VALERIA RACHELA; Esposito, Speranza; Maiuri, MARIA CHIARA; Raia, Valeria; Guido, Kroemer; Luigi, Maiuri
Targeting the Intracellular Environment in Cystic Fibrosis: Restoring Autophagy as a Novel Strategy to Circumvent the CFTR Defect.
2013 Villella, Vr; Esposito, S; Bruscia, Em; Maiuri, MARIA CHIARA; Raia, Valeria; Kroemer, G; Maiuri, L.
Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
---|---|---|---|---|
Identification of an ultra-rare Alu insertion in the CFTR gene: Pitfalls and challenges in genetic test interpretation | 1.1 Articolo in rivista | 2024 | Esposito, Speranza; Zollo, Immacolata; Villella, Valeria Rachela; Scialò, Filippo; Giordano, Sonia; Esposito, Maria Valeria; Salemme, Nunzia; Di Domenico, Carmela; Cernera, Gustavo; Zarrilli, Federica; Castaldo, Giuseppe; Amato, Felice | |
Collective rotational motion of freely expanding T84 epithelial cell colonies | 1.1 Articolo in rivista | 2023 | Ascione, Flora; Caserta, Sergio; Esposito, Speranza; Villella, Valeria Rachela; Maiuri, Luigi; Nejad, Mehrana R; Doostmohammadi, Amin; Yeomans, Julia M; Guido, Stefano | |
In silico analysis and theratyping of an ultra-rare CFTR genotype (W57G/A234D) in primary human rectal and nasal epithelial cells | 1.1 Articolo in rivista | 2023 | Kleinfelder, Karina; Lotti, Virginia; Eramo, Adriana; Amato, Felice; Lo Cicero, Stefania; Castelli, Germana; Spadaro, Francesca; Farinazzo, Alessia; Dell'Orco, Daniele; Preato, Sara; Conti, Jessica; Rodella, Luca; Tomba, Francesco; Cerofolini, Angelo; Baldisseri, Elena; Bertini, Marina; Volpi, Sonia; Villella, Valeria Rachela; Esposito, Speranza; Zollo, Immacolata; Castaldo, Giuseppe; Laudanna, Carlo; Sorsher, Eric J; Hong, Jeong; Joshi, Disha; Cutting, Garry; Lucarelli, Marco; Melotti, Paola; Sorio, Claudio | |
Immuno-Sensing at Ultra-Low Concentration of TG2 Protein by Organic Electrochemical Transistors | 1.1 Articolo in rivista | 2023 | Preziosi, Valentina; Barra, Mario; Villella, VALERIA RACHELA; Esposito, Speranza; D’Angelo, Pasquale; Luigi Marasso, Simone; Cocuzza, Matteo; Cassinese, Antonio; Guido, Stefano | |
Theratyping of the Rare CFTR Genotype A559T in Rectal Organoids and Nasal Cells Reveals a Relevant Response to Elexacaftor (VX-445) and Tezacaftor (VX-661) Combination | 1.1 Articolo in rivista | 2023 | Kleinfelder, K.; Villella, V. R.; Hristodor, A. M.; Laudanna, C.; Castaldo, G.; Amato, F.; Melotti, P.; Sorio, C. | |
Organic Electrochemical Transistor Immuno-Sensors for Spike Protein Early Detection | 1.1 Articolo in rivista | 2023 | Barra, M.; Tomaiuolo, G.; Villella, V. R.; Esposito, S.; Liboa, A.; D'Angelo, P.; Marasso, S. L.; Cocuzza, M.; Bertana, V.; Camilli, E.; Preziosi, V. | |
Anakinra restores cellular proteostasis by coupling mitochondrial redox balance to autophagy | 1.1 Articolo in rivista | 2022 | van de Veerdonk, Frank L; Renga, Giorgia; Pariano, Marilena; Bellet, Marina M; Servillo, Giuseppe; Fallarino, Francesca; De Luca, Antonella; Iannitti, Rossana G; Piobbico, Danilo; Gargaro, Marco; Manni, Giorgia; D'Onofrio, Fiorella; Stincardini, Claudia; Sforna, Luigi; Borghi, Monica; Castelli, Marilena; Pieroni, Stefania; Oikonomou, Vasileios; Villella, Valeria R; Puccetti, Matteo; Giovagnoli, Stefano; Galarini, Roberta; Barola, Carolina; Maiuri, Luigi; Della Fazia, Maria Agnese; Cellini, Barbara; Talesa, Vincenzo Nicola; Dinarello, Charles A; Costantini, Claudio; Romani, Luigina | |
Probiotics Supplements Reduce ER Stress and Gut Inflammation Associated with Gliadin Intake in a Mouse Model of Gluten Sensitivity. | 1.1 Articolo in rivista | 2021 | Ferrari, E; Monzani, R; Saverio, V; Gagliardi, M; Pańczyszyn, E; Raia, V; Villella, Vr; Bona, G; Pane, M; Amoruso, A; Corazzari, M. | |
Impaired cholesterol metabolism in the mouse model of cystic fibrosis. A preliminary study | 1.1 Articolo in rivista | 2021 | Amato, F.; Castaldo, A.; Castaldo, G.; Cernera, G.; Corso, G.; Ferrari, E.; Gelzo, M.; Monzani, R.; Villella, V. R.; Raia, V. | |
Inhaled medications in cystic fibrosis beyond antibiotics | 1.1 Articolo in rivista | 2019 | Sepe, A; Villella, Vr; Cimbalo, C; Castaldo, A; Nunziata, Francesco; Corcione, Adele; Bona, G; Maiuri, L; Raia, V | |
Defective proteostasis in celiac disease as a new therapeutic target | 1.1 Articolo in rivista | 2019 | Maiuri, L; Villella, Vr; Piacentini, Francesco; Raia, V; Kroemer, G; Raia, Valeria | |
A pathogenic role for cystic fibrosis transmembrane conductance regulator in celiac disease | 1.1 Articolo in rivista | 2019 | Villella, Vr; Venerando, A; Cozza, G; Esposito, S; Ferrari, E; Monzani, R; Spinella, Mc; Oikonomou, V; Renga, G; Tosco, A; Rossin, F; Guido, S; Silano, Angelo; Garaci, E; Chao, Yk; Grimm, C; Luciani, A; Romani, L; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L | |
Cystic fibrosis transmembrane conductance regulator (CFTR) and autophagy: hereditary defects in cystic fibrosis versus gluten-mediated inhibition in celiac disease | 1.1 Articolo in rivista | 2019 | Maiuri, L; Raia, V; Piacentini, M; Tosco, A; Villella, Vr; Kroemer, G | |
Personalization of therapies in rare diseases: a translational approach for the treatment of cystic fibrosis. | 1.1 Articolo in rivista | 2019 | Villella, Vr; Tosco, A; Esposito, S; Ferrari, E; Bona, G; Kroemer, G; Raia, V; Maiuri, L | |
Genistein antagonizes gliadin-induced CFTR malfunction in models of celiac disease. | 1.1 Articolo in rivista | 2019 | Esposito, S; Villella, Vr; Ferrari, E; Monzani, R; Tosco, A; Rossin, F; D'Eletto, M; Castaldo, A; Luciani, A; Silano, M; Bona, G; Marseglia, Gl; Romani, L; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L | |
Autophagy suppresses the pathogenic immune response to dietary antigens in cystic fibrosis. | 1.1 Articolo in rivista | 2019 | Villella, Vr; Esposito, S; Ferrari, E; Monzani, R; Tosco, A; Rossin, F; Castaldo, A; Silano, M; Marseglia, Gl; Romani, L; Barlev, Na; Piacentini, M; Raia, V; Kroemer, G; Maiuri, L | |
Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation | 1.1 Articolo in rivista | 2017 | Ferrari, Eleonora; Monzani, Romina; Villella, VALERIA RACHELA; Esposito, Speranza; Saluzzo, Francesca; Rossin, Federica; D'Eletto, Manuela; Tosco, Antonella; DE GREGORIO, Fabiola; Izzo, Valentina; Maiuri, MARIA CHIARA; Kroemer, Guido; Raia, Valeria; Maiuri, Luigi | |
Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation. | 1.1 Articolo in rivista | 2014 | Stefano, Dd; Villella, Vr; Esposito, S; Tosco, A; Sepe, A; De Gregorio, F; Salvadori, L; Grassia, R; Leone, Ca; DE ROSA, Giuseppe; Maiuri, MARIA CHIARA; Pettoello Mantovani, M; Guido, Stefano; Bossi, A; Zolin, A; Venerando, A; Pinna, La; Mehta, A; Bona, G; Kroemer, G; Maiuri, L; Raia, Valeria | |
Towards a rational combination therapy of cystic fibrosis: How cystamine restores the stability of mutant CFTR | 1.1 Articolo in rivista | 2013 | Villella, VALERIA RACHELA; Esposito, Speranza; Maiuri, MARIA CHIARA; Raia, Valeria; Guido, Kroemer; Luigi, Maiuri | |
Targeting the Intracellular Environment in Cystic Fibrosis: Restoring Autophagy as a Novel Strategy to Circumvent the CFTR Defect. | 1.1 Articolo in rivista | 2013 | Villella, Vr; Esposito, S; Bruscia, Em; Maiuri, MARIA CHIARA; Raia, Valeria; Kroemer, G; Maiuri, L. |
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