Sfoglia per Autore
Metabolic rewiring and autophagy inhibition correct lysosomal storage disease in mucopolysaccharidosis IIIB
2024 Scarcella, Melania; Scerra, Gianluca; Ciampa, Mariangela; Caterino, Marianna; Costanzo, Michele; Rinaldi, Laura; Feliciello, Antonio; Anzilotti, Serenella; Fiorentino, Chiara; Renna, Maurizio; Ruoppolo, Margherita; Pavone, Luigi Michele; D'Agostino, Massimo; De Pasquale, Valeria
N-Substituted l-Iminosugars for the Treatment of Sanfilippo Type B Syndrome
2023 De Pasquale, Valeria; Esposito, Anna; Scerra, Gianluca; Scarcella, Melania; Ciampa, Mariangela; Luongo, Antonietta; D'Alonzo, Daniele; Guaragna, Annalisa; D'Agostino, Massimo; Pavone, Luigi Michele
The Key Role of Lysosomal Protease Cathepsins in Viral Infections
2022 Scarcella, Melania; D'Angelo, Danila; Ciampa, Mariangela; Tafuri, Simona; Avallone, Luigi; Pavone, Luigi Michele; De Pasquale, Valeria
Lysosomal positioning diseases: beyond substrate storage
2022 Scerra, Gianluca; De Pasquale, Valeria; Scarcella, Melania; Caporaso, Maria Gabriella; Pavone, Luigi Michele; D'Agostino, Massimo
Editorial: Molecular Aspects of Mucopolysaccharidoses
2022 Węgrzyn, Grzegorz; Pierzynowska, Karolina; Pavone, Luigi Michele
Molecular Mechanisms in Lysosomal Storage Diseases: From Pathogenesis to Therapeutic Strategies
2022 De Pasquale, Valeria; Scarcella, Melania; Pavone, Luigi Michele
Heparan sulfate proteoglycans in viral infection and treatment: A special focus on sars-cov-2
2021 De Pasquale, V.; Quiccione, M. S.; Tafuri, S.; Avallone, L.; Pavone, L. M.
Evaluation of muscle proteins and DNA degradation to estimate the post-mortem interval in veterinary forensic pathology
2021 Piegari, G; D’Aquino, I; De Pasquale, V; Prisco, F; Baldassarre, V; De Biase, D; Tafuri, S; Pavone, Lm; Paciello, O
Early onset effects of single substrate accumulation recapitulate major features of LSD in patient-derived lysosomes
2021 Scerra, Gianluca; De Pasquale, Valeria; Pavone, Luigi Michele; Caporaso, Maria Gabriella; Mayer, Andreas; Renna, Maurizio; D'Agostino, Massimo
Competitive binding of extracellular accumulated heparan sulfate reduces lysosomal storage defects and triggers neuronal differentiation in a model of Mucopolysaccharidosis IIIB
2021 De Pasquale, V.; Scerra, G.; Scarcella, M.; D'Agostino, M.; Pavone, L. M.
Aortopathies in mouse models of Pompe, Fabry and Mucopolysaccharidosis IIIB lysosomal storage diseases
2020 Belfiore, M. P.; Iacobellis, F.; Acampora, E.; Caiazza, M.; Rubino, M.; Monda, E.; Magaldi, M. R.; Tarallo, A.; Sasso, M.; De Pasquale, V.; Grassi, R.; Cappabianca, S.; Calabro, P.; Fecarotta, S.; Esposito, S.; Esposito, G.; Pisani, A.; Pavone, L. M.; Parenti, G.; Limongelli, G.
Heparan Sulfate Proteoglycan Signaling in Tumor Microenvironment
2020 De Pasquale, Valeria; Pavone, Luigi Michele
Cathepsins in the Pathophysiology of Mucopolysaccharidoses: New Perspectives for Therapy
2020 De Pasquale, Valeria; Moles, Anna; Pavone, Luigi Michele
Targeted Metabolomic Analysis of a Mucopolysaccharidosis IIIB Mouse Model Reveals an Imbalance of Branched-Chain Amino Acid and Fatty Acid Metabolism
2020 De Pasquale, Valeria; Caterino, Marianna; Costanzo, Michele; Fedele, Roberta; Ruoppolo, Margherita; Pavone, Luigi Michele
Proteomic Analysis of Mucopolysaccharidosis IIIB Mouse Brain.
2020 De Pasquale, V; Costanzo, M; Siciliano, Ra; Mazzeo, Mf; Pistorio, V; Bianchi, L; Marchese, E; Ruoppolo, M; Pavone, Lm; Caterino, M.
Heparan sulfate proteoglycans: The sweet side of development turns sour in mucopolysaccharidoses
2019 De Pasquale, V.; Pavone, L. M.
EGFR activation triggers cellular hypertrophy and lysosomal disease in NAGLU-depleted cardiomyoblasts, mimicking the hallmarks of mucopolysaccharidosis IIIB
2018 De Pasquale, Valeria; Pezone, Antonio; Sarogni, Patrizia; Tramontano, Alfonso; Schiattarella, Gabriele Giacomo; Avvedimento, Vittorio Enrico; Paladino, Simona; Pavone, Luigi Michele
Targeting Heparan Sulfate Proteoglycans as a Novel Therapeutic Strategy for Mucopolysaccharidoses
2018 De Pasquale, Valeria; Sarogni, Patrizia; Pistorio, Valeria; Cerulo, Giuliana; Paladino, Simona; Pavone, Luigi Michele
Effect of mutated Cu, Zn Superoxide dismutase (SOD1G93A) on modulation of transductional pathway mediated by M1 muscarinic receptor in SK-N-BE and NSC-34 cells
2018 Damiano, Simona; Sasso, Anna; Accetta, Roberta; Monda, Marcellino; De Luca, Bruno; Pavone, Luigi Michele; Belfiore, Anna; Santillo, Mariarosaria; Mondola, Paolo
The Multifaceted Role of the Lysosomal Protease Cathepsins in Kidney Disease
2017 Cocchiaro, Pasquale; DE PASQUALE, Valeria; DELLA MORTE, Rossella; Tafuri, Simona; Avallone, Luigi; Pizard, Anne; Moles, Anna; Pavone, LUIGI MICHELE
Titolo | Tipologia | Data di pubblicazione | Autore(i) | File |
---|---|---|---|---|
Metabolic rewiring and autophagy inhibition correct lysosomal storage disease in mucopolysaccharidosis IIIB | 1.1 Articolo in rivista | 2024 | Scarcella, Melania; Scerra, Gianluca; Ciampa, Mariangela; Caterino, Marianna; Costanzo, Michele; Rinaldi, Laura; Feliciello, Antonio; Anzilotti, Serenella; Fiorentino, Chiara; Renna, Maurizio; Ruoppolo, Margherita; Pavone, Luigi Michele; D'Agostino, Massimo; De Pasquale, Valeria | |
N-Substituted l-Iminosugars for the Treatment of Sanfilippo Type B Syndrome | 1.1 Articolo in rivista | 2023 | De Pasquale, Valeria; Esposito, Anna; Scerra, Gianluca; Scarcella, Melania; Ciampa, Mariangela; Luongo, Antonietta; D'Alonzo, Daniele; Guaragna, Annalisa; D'Agostino, Massimo; Pavone, Luigi Michele | |
The Key Role of Lysosomal Protease Cathepsins in Viral Infections | 1.1 Articolo in rivista | 2022 | Scarcella, Melania; D'Angelo, Danila; Ciampa, Mariangela; Tafuri, Simona; Avallone, Luigi; Pavone, Luigi Michele; De Pasquale, Valeria | |
Lysosomal positioning diseases: beyond substrate storage | 1.8 Articolo in rassegna (review) | 2022 | Scerra, Gianluca; De Pasquale, Valeria; Scarcella, Melania; Caporaso, Maria Gabriella; Pavone, Luigi Michele; D'Agostino, Massimo | |
Editorial: Molecular Aspects of Mucopolysaccharidoses | 1.1 Articolo in rivista | 2022 | Węgrzyn, Grzegorz; Pierzynowska, Karolina; Pavone, Luigi Michele | |
Molecular Mechanisms in Lysosomal Storage Diseases: From Pathogenesis to Therapeutic Strategies | 1.1 Articolo in rivista | 2022 | De Pasquale, Valeria; Scarcella, Melania; Pavone, Luigi Michele | |
Heparan sulfate proteoglycans in viral infection and treatment: A special focus on sars-cov-2 | 1.1 Articolo in rivista | 2021 | De Pasquale, V.; Quiccione, M. S.; Tafuri, S.; Avallone, L.; Pavone, L. M. | |
Evaluation of muscle proteins and DNA degradation to estimate the post-mortem interval in veterinary forensic pathology | 4.2 Abstract in Atti di convegno | 2021 | Piegari, G; D’Aquino, I; De Pasquale, V; Prisco, F; Baldassarre, V; De Biase, D; Tafuri, S; Pavone, Lm; Paciello, O | |
Early onset effects of single substrate accumulation recapitulate major features of LSD in patient-derived lysosomes | 1.1 Articolo in rivista | 2021 | Scerra, Gianluca; De Pasquale, Valeria; Pavone, Luigi Michele; Caporaso, Maria Gabriella; Mayer, Andreas; Renna, Maurizio; D'Agostino, Massimo | |
Competitive binding of extracellular accumulated heparan sulfate reduces lysosomal storage defects and triggers neuronal differentiation in a model of Mucopolysaccharidosis IIIB | 1.1 Articolo in rivista | 2021 | De Pasquale, V.; Scerra, G.; Scarcella, M.; D'Agostino, M.; Pavone, L. M. | |
Aortopathies in mouse models of Pompe, Fabry and Mucopolysaccharidosis IIIB lysosomal storage diseases | 1.1 Articolo in rivista | 2020 | Belfiore, M. P.; Iacobellis, F.; Acampora, E.; Caiazza, M.; Rubino, M.; Monda, E.; Magaldi, M. R.; Tarallo, A.; Sasso, M.; De Pasquale, V.; Grassi, R.; Cappabianca, S.; Calabro, P.; Fecarotta, S.; Esposito, S.; Esposito, G.; Pisani, A.; Pavone, L. M.; Parenti, G.; Limongelli, G. | |
Heparan Sulfate Proteoglycan Signaling in Tumor Microenvironment | 1.1 Articolo in rivista | 2020 | De Pasquale, Valeria; Pavone, Luigi Michele | |
Cathepsins in the Pathophysiology of Mucopolysaccharidoses: New Perspectives for Therapy | 1.1 Articolo in rivista | 2020 | De Pasquale, Valeria; Moles, Anna; Pavone, Luigi Michele | |
Targeted Metabolomic Analysis of a Mucopolysaccharidosis IIIB Mouse Model Reveals an Imbalance of Branched-Chain Amino Acid and Fatty Acid Metabolism | 1.1 Articolo in rivista | 2020 | De Pasquale, Valeria; Caterino, Marianna; Costanzo, Michele; Fedele, Roberta; Ruoppolo, Margherita; Pavone, Luigi Michele | |
Proteomic Analysis of Mucopolysaccharidosis IIIB Mouse Brain. | 1.1 Articolo in rivista | 2020 | De Pasquale, V; Costanzo, M; Siciliano, Ra; Mazzeo, Mf; Pistorio, V; Bianchi, L; Marchese, E; Ruoppolo, M; Pavone, Lm; Caterino, M. | |
Heparan sulfate proteoglycans: The sweet side of development turns sour in mucopolysaccharidoses | 1.1 Articolo in rivista | 2019 | De Pasquale, V.; Pavone, L. M. | |
EGFR activation triggers cellular hypertrophy and lysosomal disease in NAGLU-depleted cardiomyoblasts, mimicking the hallmarks of mucopolysaccharidosis IIIB | 1.1 Articolo in rivista | 2018 | De Pasquale, Valeria; Pezone, Antonio; Sarogni, Patrizia; Tramontano, Alfonso; Schiattarella, Gabriele Giacomo; Avvedimento, Vittorio Enrico; Paladino, Simona; Pavone, Luigi Michele | |
Targeting Heparan Sulfate Proteoglycans as a Novel Therapeutic Strategy for Mucopolysaccharidoses | 1.1 Articolo in rivista | 2018 | De Pasquale, Valeria; Sarogni, Patrizia; Pistorio, Valeria; Cerulo, Giuliana; Paladino, Simona; Pavone, Luigi Michele | |
Effect of mutated Cu, Zn Superoxide dismutase (SOD1G93A) on modulation of transductional pathway mediated by M1 muscarinic receptor in SK-N-BE and NSC-34 cells | 1.1 Articolo in rivista | 2018 | Damiano, Simona; Sasso, Anna; Accetta, Roberta; Monda, Marcellino; De Luca, Bruno; Pavone, Luigi Michele; Belfiore, Anna; Santillo, Mariarosaria; Mondola, Paolo | |
The Multifaceted Role of the Lysosomal Protease Cathepsins in Kidney Disease | 1.1 Articolo in rivista | 2017 | Cocchiaro, Pasquale; DE PASQUALE, Valeria; DELLA MORTE, Rossella; Tafuri, Simona; Avallone, Luigi; Pizard, Anne; Moles, Anna; Pavone, LUIGI MICHELE |
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